SGSH/Sulphamidase Antibody, Cy7 Conjugated

Catalog number:	bs-11756R-Cy7 Buy Now
Price:	322 €
Supplier:	ABM lentivectors
Product name:	SGSH/Sulphamidase Antibody, Cy7 Conjugated
Quantity:	1.0 µg DNA
Related search:	antibody antibodies gene sulfamidase

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Long name:	Cy7 Conjugated, SGSH/Sulphamidase Polyclonal Antibody
Category:	Conjugated Primary Antibodies
Conjugation:	Cy7
Host Organism:	Rabbit (Oryctolagus cuniculus)
Target Antigen:	SGSH/Sulphamidase
Specificity:	This is a highly specific antibody against SGSH/Sulphamidase
Modification:	Unmodified
Modification site:	None
Clonality:	Polyclonal
Clone:	Polyclonal antibody
Concentration:	1ug per 1ul
Immunogen_range:	310-360/502
Subcellular location:	Lysosome
Source:	KLH conjugated synthetic peptide derived from human Sulphamidase
Gene ID number:	6448
Swiss Prot:	P51688
Tested applications:	IF(IHC-P)
Recommended dilutions:	IF(IHC-P)(1:50-200)
Crossreactivity:	Mouse, Rat, Human
Crossreactive species details:	not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Antigen background:	Defects in the gene encoding sulfamidase are the cause of Sanfilippo syndrome A, Deficiency of lysosomal sulfatases leads to human diseases characterized by the accumulation of either GAGs (glycosaminoglycans) or sulfolipids, It has been suggested that sulfamidase may be involved in the lysosomal degradation of heparan sulfate, MPS3A or SGSH, SFMD, Sanfilippo syndrome A is characterized by severe central nervous system degeneration but relatively mild somatic manifestations, Sulfamidase, also known as HSS, an autosomal recessive lysosomal storage disease caused by impaired degradation of heparan sulfate, is a 502 amino acid lysosome that belongs to the sulfatase family, Sulfatases are enzymes that hydrolyse a diverse range of sulfate esters
Purification method:	This antibody was purified via Protein A
Storage conditions:	50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA
Excitation Emission:	743nm/767nm
Synonyms:	HSS MPS3A SFMD
Properties:	C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24°
Conjugated:	These antibodies are excite for emission at 650 nm and detected at a 676 nm wavelengths
Gene target:	SGSH/Sulphamidase Conjugated
Short name:	Conjugated, SGSH/Sulphamidase Antibody
Technique:	antibodies against human proteins, antibodies for, antibody Conjugates, Antibody
Label:	Cy7
Alternative name:	cyanine 7 coupled, SGSH/Sulphamidase (Antibody to)
Alternative technique:	antibodies
Identity:	10818
Gene:	SGSH | More about : SGSH
Long gene name:	N-sulfoglucosamine sulfohydrolase
Synonyms name:	sulfamidase mucopolysaccharidosis type IIIA
Locus:	17q25, 3
Discovery year:	1997-06-24
GenBank acession:	BC047318
Entrez gene record:	6448
Pubmed identfication:	7493035
RefSeq identity:	NM_000199
Classification:	Sulfatases
Havana BLAST/BLAT:	OTTHUMG00000177569

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• #antibodies
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• #sulfamidase