SGSH/Sulphamidase Antibody, ALEXA FLUOR 555

Catalog number:	bs-11756R-A555 Buy Now
Price:	322 €
Supplier:	ABM lentivectors
Product name:	SGSH/Sulphamidase Antibody, ALEXA FLUOR 555
Quantity:	1.0 µg DNA
Related search:	alexa antibody fluor gene conjugated sulfamidase storage synonyms

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Long name:	ALEXA FLUOR 555 Conjugated, SGSH/Sulphamidase Polyclonal Antibody
Also known as:	Anti-SGSH/Sulphamidase PAb ALEXA FLUOR 555
Category:	Conjugated Primary Antibodies
Conjugated with:	555, ALEXA FLUOR®
Host Organism:	Rabbit (Oryctolagus cuniculus)
Target Antigen:	SGSH/Sulphamidase
Specificity:	This is a highly specific antibody against SGSH/Sulphamidase
Modification:	Unmodified
Modification Site:	None
Clonality:	Polyclonal
Clone:	Polyclonal antibody
Concentration:	1ug per 1ul
Immunogen range:	310-360/502
Subcellular location:	Lysosome
Source:	This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human Sulphamidase
Gene ID Number:	6448
Swiss Prot:	P51688
Tested applications:	IF(IHC-P)
Recommended dilutions:	IF(IHC-P)(1:50-200)
Crossreactivity:	Mouse, Rat, Human
Cross-reactive species details:	not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the antigen:	Defects in the gene encoding sulfamidase are the cause of Sanfilippo syndrome A, Deficiency of lysosomal sulfatases leads to human diseases characterized by the accumulation of either GAGs (glycosaminoglycans) or sulfolipids, It has been suggested that sulfamidase may be involved in the lysosomal degradation of heparan sulfate, MPS3A or SGSH, SFMD, Sanfilippo syndrome A is characterized by severe central nervous system degeneration but relatively mild somatic manifestations, Sulfamidase, also known as HSS, an autosomal recessive lysosomal storage disease caused by impaired degradation of heparan sulfate, is a 502 amino acid lysosome that belongs to the sulfatase family, Sulfatases are enzymes that hydrolyse a diverse range of sulfate esters
Purification:	Purified by Protein A
Storage conditions:	50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA
Excitation emission:	553nm/568nm
Synonyms:	HSS MPS3A SFMD
Properties:	ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, Very high photo stable ALEXA conjugate, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate
Conjugation:	ALEXA FLUOR 555, Alexa Fluor
Gene target:	SGSH/Sulphamidase
Short name:	SGSH/Sulphamidase Antibody
Technique:	antibodies against human proteins, antibodies for, Antibody
Label:	ALEXA FLUOR 555
Alternative name:	ALEXA FLUOR 555, SGSH/Sulphamidase (Antibody to)
Alternative technique:	antibodies
Identity:	10818
Gene:	SGSH | More about : SGSH
Long gene name:	N-sulfoglucosamine sulfohydrolase
Synonyms name:	sulfamidase mucopolysaccharidosis type IIIA
Locus:	17q25, 3
Discovery year:	1997-06-24
GenBank acession:	BC047318
Entrez gene record:	6448
Pubmed identfication:	7493035
RefSeq identity:	NM_000199
Classification:	Sulfatases
Havana BLAST/BLAT:	OTTHUMG00000177569

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