| Long name: |
Cy3 Conjugated, HMBS Polyclonal Antibody |
| Category: |
Conjugated Primary Antibodies |
| Conjugation: |
cy3 conjugation kit |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
HMBS |
| Specificity: |
This is a highly specific antibody against HMBS |
| Modification: |
Unmodified |
| Modification site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
KLH conjugated synthetic peptide derived from human HMBS/PBGD |
| Gene ID number: |
3145 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Mouse, Rat, Human |
| Crossreactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Antigen background: |
AIP is characterized by acute attacks of neurological dysfunctions with hypertension, Deficiency of PBGD causes errors in pyrrole metabolism, PBGD belongs to the HMBS (hydroxymethylbilane synthase) family, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine, also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway, peripheral neurologic disturbances, tachycardia, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP), PBGD |
| Purification method: |
This antibody was purified via Protein A |
| Storage conditions: |
50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA |
| Excitation Emission: |
512, 550nm/570, 615nm |
| Properties: |
1 of the HMBS Antibody, Conjugated can be used in flow cytometry but typically shows lower fluorescence intensity comparable to that of PE or APC, Cy3 antibodies are excited by the 488-nanometer wave of an argon laser and the 633-nanometer line of a helium-neon diode laser, This Bioss Primary Conjugated Antibodies antibody is well suited for fluorescent microscopy, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24° |
| Gene target: |
HMBS Conjugated |
| Short name: |
Conjugated, HMBS Antibody |
| Technique: |
antibodies against human proteins, antibodies for, antibody Conjugates, Antibody |
| Label: |
Cy3 |
| Alternative name: |
cyanine 3 coupled, HMBS (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
4982 |
| Gene: |
HMBS |
More about : HMBS |
| Long gene name: |
hydroxymethylbilane synthase |
| Synonyms gene: |
PBGD UPS PORC |
| Synonyms gene name: |
Chester type , acute, uroporphyrinogen I synthase porphobilinogen deaminase porphyria |
| Locus: |
11q23, 3 |
| Discovery year: |
1986-01-01 |
| GenBank acession: |
X04808 |
| Entrez gene record: |
3145 |
| Pubmed identfication: |
8432552 17298217 |
| RefSeq identity: |
NM_000190 |
| Havana BLAST/BLAT: |
OTTHUMG00000168295 |
| Locus Specific Databases: |
LRG_1076 |