| Long name: |
ALEXA FLUOR 555 Conjugated, HIBCH Polyclonal Antibody |
| Also known as: |
Anti-HIBCH PAb ALEXA FLUOR 555 |
| Category: |
Conjugated Primary Antibodies |
| Conjugated with: |
555, ALEXA FLUOR® |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
HIBCH |
| Specificity: |
This is a highly specific antibody against HIBCH |
| Modification: |
Unmodified |
| Modification Site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human HIBCH |
| Gene ID Number: |
26275 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Human |
| Cross-reactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Background of the antigen: |
Defects to this gene result in HIBCH deficiency (HIBCHD), Existing as two alternatively spliced isoforms, HIBCH hydrolyzes HIBYL-CoA, HIBCH is highly expressed in liver and kidney, HIBCHD is characterized by the accumulation of methacrylyl-CoA, Localizing to the mitochondria, Phenotypic symptoms include early deterioration of neurological function, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups, a saline catabolite, an intermediate in the minor pathway involved in the metabolism of proprionate, and Î, delayed motor skill development and hypotonia, known alternatively as deficiency of Î, muscle and brain, the gene encoding HIBCH maps to human chromosome 2q32, with lower levels found in heart, ², ², -hydroxyisobutyryl CoA deacylase or methacrylic aciduria, -hydroxypropionyl-CoA, 2, HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family |
| Purification: |
Purified by Protein A |
| Storage conditions: |
50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA |
| Excitation emission: |
553nm/568nm |
| Properties: |
ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, Very high photo stable ALEXA conjugate, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate |
| Conjugation: |
ALEXA FLUOR 555, Alexa Fluor |
| Gene target: |
HIBCH |
| Short name: |
HIBCH Antibody |
| Technique: |
antibodies against human proteins, antibodies for, Antibody |
| Label: |
ALEXA FLUOR 555 |
| Alternative name: |
ALEXA FLUOR 555, HIBCH (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
4908 |
| Gene: |
HIBCH |
More about : HIBCH |
| Long gene name: |
3-hydroxyisobutyryl-CoA hydrolase |
| Synonyms gene name: |
3-hydroxyisobutyryl-Coenzyme A hydrolase |
| Locus: |
2q32, 2 |
| Discovery year: |
1999-12-07 |
| GenBank acession: |
U66669 |
| Entrez gene record: |
26275 |
| Pubmed identfication: |
8824301 |
| Havana BLAST/BLAT: |
OTTHUMG00000132673 |