Myotilin Antibody, ALEXA FLUOR 350

Catalog number:	bs-6479R-A350 Buy Now
Price:	332 €
Supplier:	Bioss Primary Conjugated Antibodies.
Product name:	Myotilin Antibody, ALEXA FLUOR 350
Quantity:	100ul
Related search:	myotilin alexa gene antibody antibodies lgmd human synonyms year

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Long name:	ALEXA FLUOR 350 Conjugated, Myotilin Polyclonal Antibody
Also known as:	Anti-Myotilin PAb ALEXA FLUOR 350
Category:	Conjugated Primary Antibodies
Conjugated with:	350, ALEXA FLUOR®
Host Organism:	Rabbit (Oryctolagus cuniculus)
Target Antigen:	Myotilin
Specificity:	This is a highly specific antibody against Myotilin
Modification:	Unmodified
Modification Site:	None
Clonality:	Polyclonal
Clone:	Polyclonal antibody
Concentration:	1ug per 1ul
Source:	This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human Myotilin
Gene ID Number:	9499
Tested applications:	IF(IHC-P)
Recommended dilutions:	IF(IHC-P)(1:50-200)
Crossreactivity:	Mouse, Rat, Human
Cross-reactive species details:	not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the antigen:	Defects in the myotilin gene are reported to cause a form of autosomal dominant limb-girdle muscular dystrophy (LGMD), Myotilin is expressed in skeletal and cardiac muscle, Symptoms of adult onset LGMD are progressive weakness of the hip and shoulder girdles as well as a distinctive dysarthric pattern of speech, The muscle of affected individuals with LGMD shows degeneration of myofibers, a sarcomeric protein that is encoded by the gene mapping to human chromosome 5q31, and it co-localizes with a-actinin in the sarcomeric I-bands where it directly interacts with a-actinin, binds to a-actinin and is localized in the Z-line of myofibrils, centrally located myonuclei and an enhanced number of autophagic vesicles, fiber splitting, variations in fiber size, Myotilin
Purification:	Purified by Protein A
Storage conditions:	50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA
Excitation emission:	343nm/442nm
Synonyms:	MYOT
Properties:	ALEXA FLUOR they should be stored frozen at - 24°, Alexa Fluor 350 conjugates can be used in multi-color flow cytometry with FACS's equipped with a second red laser or red diode, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate
Conjugation:	ALEXA FLUOR 350, Alexa Fluor
Gene target:	Myotilin
Short name:	Myotilin Antibody
Technique:	antibodies against human proteins, antibodies for, Antibody
Label:	ALEXA FLUOR 350
Alternative name:	ALEXA FLUOR 350, Myotilin (Antibody to)
Alternative technique:	antibodies
Identity:	6573
Gene:	LGMD1 | More about : LGMD1
Long gene name:	myotilin
Synonyms gene:	TTID LGMD1A
Synonyms gene name:	titin immunoglobulin domain protein (myotilin) limb-girdle muscular dystrophy 1A (autosomal dominant)
Locus:	5q31, 2
Discovery year:	1999-04-16
GenBank acession:	AF133820
Entrez gene record:	9499
Pubmed identfication:	10486214 10369880
RefSeq identity:	NM_006790
Classification:	I-set domain containing
Havana BLAST/BLAT:	OTTHUMG00000129154
Locus Specific Databases:	Myotilin (TTID) sequence variations Leiden Muscular Dystrophy pages LRG_201

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