| Long name: |
FITC Conjugated, HIBADH Polyclonal Antibody |
| Category: |
Conjugated Primary Antibodies |
| Conjugation: |
Anti-FITC Antibody |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
HIBADH |
| Specificity: |
This is a highly specific antibody against HIBADH |
| Modification: |
Unmodified |
| Modification site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
KLH conjugated synthetic peptide derived from human HIBADH |
| Gene ID number: |
11112 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Human |
| Crossreactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Antigen background: |
However, It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, The enzyme functions as a homodimer between a pH of 7, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features, an intermediate of valine catabolism, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, with optimal activity between 8, 0 and 10, 8 and 9, HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent |
| Purification method: |
This antibody was purified via Protein A |
| Storage conditions: |
50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA |
| Excitation Emission: |
494nm/518nm |
| Synonyms: |
NS5ATP1 |
| Properties: |
Bioss Primary Conjugated Antibodies FITC is highly sensitive to pH extremes, FITC has a green emission that's usually collected at 530 nanometers, FITC has a high quantum yield (efficiency of energy transfer from absorption to emission fluorescence) and approximately half of the absorbed photons are emitted as fluorescent light, For fluorescent microscopy applications, This Bioss Primary Conjugated Antibodies Fluorescein isothiocyanate (FITC) antibody is currently after some BD antibodies the most commonly used fluorescent dye for FACS, When excited at 488 nanometers, its photo bleaching effects are not observed due to a very brief interaction at the laser intercept, the 1 FITC is seldom used as it photo bleaches rather quickly though in flow cytometry applications, the FL1 detector of a FACSCalibur or FACScan, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24° |
| Gene target: |
HIBADH Conjugated |
| Short name: |
FITC Conjugated, HIBADH Antibody |
| Technique: |
Fluorescein, antibodies against human proteins, antibodies for, antibody Conjugates, Antibody |
| Label: |
FITC |
| Alternative name: |
fluorecein coupled, HIBADH (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
4907 |
| Gene: |
HIBADH |
More about : HIBADH |
| Long gene name: |
3-hydroxyisobutyrate dehydrogenase |
| Locus: |
7p15, 2 |
| Discovery year: |
1999-08-05 |
| GenBank acession: |
AF529362 |
| Entrez gene record: |
11112 |
| RefSeq identity: |
NM_152740 |
| Havana BLAST/BLAT: |
OTTHUMG00000097035 |