| Long name: |
ALEXA FLUOR 350 Conjugated, HIBADH Polyclonal Antibody |
| Also known as: |
Anti-HIBADH PAb ALEXA FLUOR 350 |
| Category: |
Conjugated Primary Antibodies |
| Conjugated with: |
350, ALEXA FLUOR® |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
HIBADH |
| Specificity: |
This is a highly specific antibody against HIBADH |
| Modification: |
Unmodified |
| Modification Site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human HIBADH |
| Gene ID Number: |
11112 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Human |
| Cross-reactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Background of the antigen: |
However, It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, The enzyme functions as a homodimer between a pH of 7, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features, an intermediate of valine catabolism, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, with optimal activity between 8, 0 and 10, 8 and 9, HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent |
| Purification: |
Purified by Protein A |
| Storage conditions: |
50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA |
| Excitation emission: |
343nm/442nm |
| Synonyms: |
NS5ATP1 |
| Properties: |
ALEXA FLUOR they should be stored frozen at - 24°, Alexa Fluor 350 conjugates can be used in multi-color flow cytometry with FACS's equipped with a second red laser or red diode, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate |
| Conjugation: |
ALEXA FLUOR 350, Alexa Fluor |
| Gene target: |
HIBADH |
| Short name: |
HIBADH Antibody |
| Technique: |
antibodies against human proteins, antibodies for, Antibody |
| Label: |
ALEXA FLUOR 350 |
| Alternative name: |
ALEXA FLUOR 350, HIBADH (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
4907 |
| Gene: |
HIBADH |
More about : HIBADH |
| Long gene name: |
3-hydroxyisobutyrate dehydrogenase |
| Locus: |
7p15, 2 |
| Discovery year: |
1999-08-05 |
| GenBank acession: |
AF529362 |
| Entrez gene record: |
11112 |
| RefSeq identity: |
NM_152740 |
| Havana BLAST/BLAT: |
OTTHUMG00000097035 |