| Long name: |
Biotin Conjugated, Alpha Glucosidase Polyclonal Antibody |
| Category: |
Conjugated Primary Antibodies |
| Conjugation: |
Biotinylated |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
GAA |
| Specificity: |
This is a highly specific antibody against GAA |
| Modification: |
Unmodified |
| Modification site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
KLH conjugated synthetic peptide derived from human GAA/Glucosidase alpha |
| Gene ID number: |
2548 |
| Tested applications: |
IHC-P, WB |
| Recommended dilutions: |
IHC-P(1:100-500), WB(1:100-1000) |
| Crossreactivity: |
Mouse, Rat, Human |
| Crossreactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Antigen background: |
Defects in this gene are the cause of glycogen storage disease II, Different forms of acid alpha-glucosidase are obtained by proteolytic processing, Jul 2008], Three transcript variants encoding the same protein have been found for this gene, [provided by RefSeq, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum, which is essential for the degradation of glycogen to glucose in lysosomes, This gene encodes acid alpha-glucosidase |
| Purification method: |
This antibody was purified via Protein A |
| Storage conditions: |
50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA |
| Synonyms: |
Acid alpha glucosidase, Acid maltase, Aglucosidase alfa, Alpha glucosidase, GAA, Glucosidase alpha, Glucosidase alpha acid, Glucosidase alpha acid Pompe disease glycogen storage disease type II, LYAG, LYAG_HUMAN, Lysosomal alpha glucosidase, 70 kDa lysosomal alpha-glucosidase |
| Description: |
Conjugated is a &alpha, - or alpha protein sometimes glycoprotein present in blood, The Alpha Glucosidase Antibody |
| Properties: |
Avidin and Streptavidin bind to the small biotin and are couple to HRP or AP for ELISA, Biotin conjugates can be detected by horseradish peroxidase, To break the streptavidin Biotin bond we suggest to use a 6 molar guanidine HCl solution with acidity of pH 1, alkaline phosphatase substrates or anti biotin conjugated antibodies, 6, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24° |
| Gene target: |
Alpha Glucosidase Conjugated |
| Short name: |
Conjugated, Alpha Glucosidase Antibody |
| Technique: |
antibodies against human proteins, antibodies for, antibody Conjugates, Antibody |
| Label: |
Biotin |
| Alternative name: |
biotinilated coupled, a Glucosidase (Antibody to) |
| Alternative technique: |
antibodies |