| Gene info: |
<, <, = ADP + phosphate + (S)-methylmalonyl-CoA, PA-1 is a life-threatening disease characterized by episodic vomiting, and intolerance to protein, developmental retardation, hypo&, lethargy and ketosis, neutropenia, periodic thrombocytopenia, subunits, subunits and six &, #946, #947, <, <, -<, /b>, /b>, /b>, /sub>, /sup>, 3<, : ATP + propanoyl-CoA + HCO<, : Defects in PCCA are the cause of propionic acidemia type I (PA-1) [MIM:606054], : Probably a dodecamer composed of six biotin-containing a, CATALYTIC ACTIVITY<, DISEASE<, SUBUNIT<, b>, b>, b>, globulinemia, sub>, sup> |
| Gene names: |
PCCase alpha subunit, Propanoyl-CoA:carbon dioxide ligase alpha subunit, PropionylCoA carboxylase alpha chain, mitochondrial, mitochondrialPCCase subunit alpha, Propionyl-CoA carboxylase alpha chain |
| Antibodie's label: |
unlabelled serum |
| Purity: |
Immunoaffinity Purified |
| Ab raised in: |
Chicken |
| Type: |
Polyclonal |
| Antigen: |
450-703 |
| Immuno application: |
Western Blot |
| Antibody advice: |
chain, chain, mitochondrial antibody can be used for the detection of Propionyl-CoA carboxylase a, mitochondrial by Western Blot, Propionyl-CoA carboxylase a |
| Suspention, pH, azide: |
No preservatives added, Phosphate-Buffered Saline |
| Keep at: |
Antibodies should not be exposed to prolonged high temperatures, As with all antibodies care should be taken to avoid repeated freeze thaw cycles, Long term storage should be at -20 grades C, PCCA antibody can be stored at 4 grades C for short term (weeks) |
| Works with: |
Human |
| Omim nr: |
4557833 |
| Ncbi nr: |
1, NP_000273 |
| KDa: |
4 kDa (calculated), 77 |
| Vial with antibody: |
in solution |
| Quantity per ml: |
1 mg/mL |
| NCBI GENE nr: |
5095 |
| GENE symbol: |
PCCA |
| Antigene name: |
alpha polypeptide, propionyl CoA carboxylase |
| Source: |
Homo sapiens |
| Protein nr: |
P05165 |
| Description: |
Freeze thaw will destroy a percentage in every cycle and should be avoided, C in a fridge short term in a concentrated dilution, This antibody needs to be stored at + 4° |
| Properties: |
C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by proscience they should be stored frozen at - 24° |
| Gene target: |
PCCA |
| Short name: |
anti-PCCA Antibody |
| Technique: |
antibodies against human proteins, antibodies for, antibody to, Antibody |
| Alternative name: |
antibody to-PCCA (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
8653 |
| Gene: |
PCCA |
More about : PCCA |
| Long gene name: |
propionyl-CoA carboxylase alpha subunit |
| Synonyms gene name: |
alpha polypeptide , propionyl Coenzyme A carboxylase |
| Locus: |
13q32, 3 |
| Discovery year: |
1986-01-01 |
| GenBank acession: |
X14608 |
| Entrez gene record: |
5095 |
| Pubmed identfication: |
1427880 |
| Havana BLAST/BLAT: |
OTTHUMG00000017284 |
| Locus Specific Databases: |
Propionyl CoA Carboxylase Page |