| Long name: |
Cy3 Conjugated, Galactosidase alpha Polyclonal Antibody |
| Category: |
Conjugated Primary Antibodies |
| Conjugation: |
cy3 conjugation kit |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
Galactosidase alpha |
| Specificity: |
This is a highly specific antibody against Galactosidase alpha |
| Modification: |
Unmodified |
| Modification site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Immunogen_range: |
127-148/429 |
| Subcellular location: |
Lysosome |
| Source: |
KLH conjugated synthetic peptide derived from human Galactosidase alpha |
| Gene ID number: |
2717 |
| Swiss Prot: |
P06280 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Mouse, Rat, Human |
| Crossreactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Antigen background: |
Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk, Death results from renal failure, Defects in GLA are the cause of Fabry's disease (FD), FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues, Heterozygous females may exhibit the disorder in an attenuated form, Patients may show ocular deposits, and burning pain in the extremities, cardiac or cerebral complications of hypertension or other vascular disease, febrile episodes, galactomannans and galactohydrolase, including galactose oligosaccharides, non reducing alpha D galactose residues in alpha D galactosides, they are more likely to show corneal opacities, Galactosidase alpha is involved in the hydrolysis of terminal |
| Purification method: |
This antibody was purified via Protein A |
| Storage conditions: |
50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA |
| Excitation Emission: |
512, 550nm/570, 615nm |
| Synonyms: |
Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Alpha-galactosidase A, GLA, Melibiase, GALA |
| Properties: |
1 of the Galactosidase alpha Antibody, Conjugated can be used in flow cytometry but typically shows lower fluorescence intensity comparable to that of PE or APC, Cy3 antibodies are excited by the 488-nanometer wave of an argon laser and the 633-nanometer line of a helium-neon diode laser, This Bioss Primary Conjugated Antibodies antibody is well suited for fluorescent microscopy, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24° |
| Gene target: |
Galactosidase alpha Conjugated |
| Short name: |
Conjugated, Galactosidase alpha Antibody |
| Technique: |
antibodies against human proteins, antibodies for, antibody Conjugates, Antibody |
| Label: |
Cy3 |
| Alternative name: |
cyanine 3 coupled, Galactosidase a (Antibody to) |
| Alternative technique: |
antibodies |