OTC Antibody

Catalog number:	bs-6724R Buy Now
Price:	1929 €
Supplier:	MBS Recombinant Proteins
Product name:	OTC Antibody
Quantity:	100ug
Other quantities:	1 vial 521€ 1 x 1 vial 411€ 100ul 426€
Related search:	otc antibody antibodies ornithine short

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Long name:	OTC Primary Polyclonal Antibody
Also known as:	OTC PAb
Category:	Primary Antibodies
Conjugation:	Unconjugated
Target Antigen:	OTC
Specificity:	This is a highly specific antibody against OTC
Modification(s):	None
Modification site(s):	Unmodified antibody
Clonality:	Polyclonal antibody
Clone number:	Polyclonal antibody
Concentration:	1ug per 1ul
Immunogen range:	40-90/354
Subcellular location:	Mitochondrion
Source:	This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human OTC
Gene ID number:	5009
Swiss Prot:	P00480
Tested Applications:	IF(IHC-P), IHC-P, WB
Recommended dilutions:	IF(IHC-P)(1:50-200), IHC-P(1:100-500), WB(1:100-1000)
Cross reactivity:	Mouse, Rat, Human
Cross reactive species details:	not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Background of the target antigen:	Heterozygous females are either asymptomatic or express orotic aciduria spontaneously or after protein intake, Mutations with no residual enzyme activity are always expressed in hemizygote males by a very severe neonatal hyperammonemic coma that generally proves to be fatal, OTCD is an X-linked disorder of the urea cycle which causes a form of hyperammonemia, The arbitrary classification of patients into the 'neonatal' group (clinical hyperammonemia in the first few days of life) and 'late' onset (clinical presentation after the neonatal period) has been used to differentiate severe from mild forms, The disorder is treatable with supplemental dietary arginine and low protein diet, Defects in OTC are the cause of ornithine carbamoyltransferase deficiency (OTCD) [MIM:311250]
Purification method:	This antibody was purified via Protein A
Storage conditions:	50% glycerol and 0, Store at -20°, 09% sodium azide, C for up to 1 year, Keep the antibody in aqueous buffered solution containing 1% BSA
Synonym names:	OTC, OTCase, Ornithine carbamoyltransferase, Ornithine transcarbamylase, mitochondrial, OCTD
Properties:	C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Unconjugated Antibodies they should be stored frozen at - 24°
Gene target:	OTC
Short name:	OTC Antibody
Technique:	antibodies against human proteins, antibodies for, Antibody
Alternative name:	OTC (Antibody to)
Alternative technique:	antibodies
Identity:	8512
Gene:	OTC | More about : OTC
Long gene name:	ornithine carbamoyltransferase
Locus:	Xp11, 4
Discovery year:	2001-06-22
GenBank acession:	K02100
Entrez gene record:	5009
Havana BLAST/BLAT:	OTTHUMG00000022727
Locus Specific Databases:	OTC - Ornithine transcarbamylase deficiency Mental Retardation database LOVD - Leiden Open Variation Database

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