| Long name: |
ALEXA FLUOR 555 Conjugated, HMGCL Polyclonal Antibody |
| Also known as: |
Anti-HMGCL PAb ALEXA FLUOR 555 |
| Category: |
Conjugated Primary Antibodies |
| Conjugated with: |
555, ALEXA FLUOR® |
| Host Organism: |
Rabbit (Oryctolagus cuniculus) |
| Target Antigen: |
HMGCL |
| Specificity: |
This is a highly specific antibody against HMGCL |
| Modification: |
Unmodified |
| Modification Site: |
None |
| Clonality: |
Polyclonal |
| Clone: |
Polyclonal antibody |
| Concentration: |
1ug per 1ul |
| Source: |
This antibody was obtained by immunization of the host with KLH conjugated synthetic peptide derived from human HMGCL |
| Gene ID Number: |
2835 |
| Tested applications: |
IF(IHC-P) |
| Recommended dilutions: |
IF(IHC-P)(1:50-200) |
| Crossreactivity: |
Mouse, Rat, Human |
| Cross-reactive species details: |
not every possible cross-reactivity is known, Due to limited amount of testing and knowledge |
| Background of the antigen: |
Defects in HMGCL are the cause of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency (hydroxymethylglutaricaciduria), It has a role in ketogenesis and leucine catabolism, an autosomal recessive disease which can lead to hypoglycemia and coma, liver and lymphoblasts, Hydroxymethylglutaryl-CoA lyase (HMGCL) is found in fibroblasts |
| Purification: |
Purified by Protein A |
| Storage conditions: |
50% glycerol and 0, Keep refrigerated at 2 to 8 degrees Celcius for up to one year, 09% sodium azide, Store this antibody in aqueous buffered solution containing 1% BSA |
| Excitation emission: |
553nm/568nm |
| Synonyms: |
HL |
| Properties: |
ALEXA FLUOR they should be stored frozen at - 24°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies, Very high photo stable ALEXA conjugate, C, C for long term storage and for short term at + 5°, For facs or microscopy Alexa 1 conjugate |
| Conjugation: |
ALEXA FLUOR 555, Alexa Fluor |
| Gene target: |
HMGCL |
| Short name: |
HMGCL Antibody |
| Technique: |
antibodies against human proteins, antibodies for, Antibody |
| Label: |
ALEXA FLUOR 555 |
| Alternative name: |
ALEXA FLUOR 555, HMGCL (Antibody to) |
| Alternative technique: |
antibodies |
| Identity: |
5005 |
| Gene: |
HMGCL |
More about : HMGCL |
| Long gene name: |
3-hydroxymethyl-3-methylglutaryl-CoA lyase |
| Synonyms gene name: |
3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase |
| Synonyms name: |
hydroxymethylglutaricaciduria |
| Locus: |
1p36, 11 |
| Discovery year: |
1993-12-13 |
| GenBank acession: |
BC010570 |
| Entrez gene record: |
3155 |
| Pubmed identfication: |
8102917 8978493 |
| RefSeq identity: |
NM_000191 |
| Havana BLAST/BLAT: |
OTTHUMG00000002963 |