Fumarate hydratase/FH Antibody, Biotin Conjugated

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Catalog number: bs-3938R-Biotin
Price: 2829 €
Supplier: MBS Recombinant Proteins
Product name: Fumarate hydratase/FH Antibody, Biotin Conjugated
Quantity: 100ug
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More details :

Long name: Biotin Conjugated, Fumarate hydratase/FH Antibody
Category: Conjugated Primary Antibodies
Conjugation: Biotinylated
Host Organism: Rabbit (Oryctolagus cuniculus)
Target Antigen: Fumarate hydratase/FH
Specificity: This is a highly specific antibody against Fumarate hydratase/FH
Modification: Unmodified
Modification site: None
Clonality: Polyclonal
Clone: Polyclonal antibody
Concentration: 1ug per 1ul
Source: KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
Gene ID number: 2271
Tested applications: IHC-P, WB
Recommended dilutions: IHC-P(1:100-500), WB(1:100-1000)
Crossreactivity: Mouse, Rat, Human
Crossreactive species details: not every possible cross-reactivity is known, Due to limited amount of testing and knowledge
Antigen background: FHD is characterized by progressive encephalopathy, cerebral atrophy and lactic and pyruvic acidemia, developmental delay, hypotonia, Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria
Purification method: This antibody was purified via Protein A
Storage conditions: 50% glycerol and 0, Store refrigerated at 2 to 8 degrees Celcius for up to 1 year, 09% sodium azide, Keep the antibody in an aqueous buffered solution containing 1% BSA
Synonyms: FH, FUMH_HUMAN, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata, mitochondrial
Properties: Avidin and Streptavidin bind to the small biotin and are couple to HRP or AP for ELISA, Biotin conjugates can be detected by horseradish peroxidase, To break the streptavidin Biotin bond we suggest to use a 6 molar guanidine HCl solution with acidity of pH 1, alkaline phosphatase substrates or anti biotin conjugated antibodies, 6, C, C for long term storage and for short term at + 5°, If you buy Antibodies supplied by Bioss Primary Conjugated Antibodies they should be stored frozen at - 24°
Gene target: Fumarate hydratase/FH Conjugated
Short name: Conjugated, Fumarate hydratase/FH Antibody
Technique: antibodies against human proteins, antibodies for, antibody Conjugates, Antibody
Label: Biotin
Alternative name: biotinilated coupled, Fumarate hydratase/FH (Antibody to)
Alternative technique: antibodies

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